Sensorineural hearing deficit

The cause of (pediatric) sensorineural hearing loss is diverse, comprising genetic, acquired, and idiopathic conditions. Identifying the specific cause requires otolaryngologic and audiometric evaluations. These generally include laboratory tests and temporal bone imaging studies. A sequential diagnostic approach has been shown to be both prudent and cost-effective. Although a definitive cause is being established, amplification and a comprehensive treatment strategy should be initiated to ensure that developmental, auditory, and speech and language delays are minimized.

Last modified
15 July 2020


Perceptive deafness

Sensorineural hearing loss (disorder)

Perceptive hearing loss

Sensorineural deafness

Sensory-neural deafness



Sensorineural hearing loss, bilateral

Rare Condition

Alport Syndrome

Alport syndrome is a hereditary renal disease, glomerulonephritis, resulting in renal failure. In addition, there is often (sensorineural) deafness and a congenital anomaly of the eye...

Coffin Lowry Syndrome

Coffin Lowry syndrome is a rare genetic disorder characterized by

  • mental retardation;
  • abnormalities of the head and facial (craniofacial) area;
  • large, soft hands with short...
General Medical Guideline