Ear (malformed (small) external ear)

Malformed external ear

Auricular abnormalities found included microtia, preauricular appendages, ear lobe and external auditory canal agenesis, anotia, malformed ossicular chains, malformed ossicles and reduced oval window.

In the middle ear, it is common to find anomalies in the ossicular chain and otitis media with effusion. Inner ear abnormalities can also occur, affecting the cochlea and semi-circular canals.

A malformed external ear occurs in different grades. We speak of Microtia when the external ear is smaller than normal.

Last modified
2 January 2021

A malformation of the external ear can be seen on ultrasound during pregnancy but for sure at birth. Malformed Auricles may occur in:

Rare Condition

Treacher Collins Syndrome

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Oculo-Auriculo-Vertebral Spectrum (Goldenhar Syndrome)

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Congenital deformity where the pinna (external ear) is underdeveloped. A...

The auditory canal is closed or absent (ICD 10 Q16.1)...